Intestinal Obstruction Due to Fibromuscular Dysplasia

Abstract

INTRODUCTION : We describe a rare case of     small bowel infarction caused by fibro muscular dysplasia   with  a good prognosis CASE PRESENTATION : We present a case, where an elderly male presented  with cardinal       symptoms and signs of intestinal obstruction. Necessary  investigations were done which concluded small bowel    infarction. Exploratory laparotomy revealed jejunal gangrene. Resection   anastamosis done. Histopathology  was     suggestive of Fibro muscular dysplasia (FMD). Post operative period   was    uneventful  and  he  was discharged  with    antiplatelets with regular follow up. Disease specific        investigations to rule out cerebral vessel involvement were all negative. Thus  the   diagnosis of ischemic bowel disease  produced probably by Fibro muscular dysplasia was made. CONCLUSION : This case illustrated the importance of    consideration of   mesentric artery FMD and cause specific treatment should be tailored to any case of intestinal        obstruction to prevent recurrences. Owing to its rarity,      mesenteric vessel FMD still eludes the surgeon in making      a diagnosis. Hence a  high degree of   suspicion is important for appropriate management.