A Rare Case of Ohvira / Herlyn Werner Wunderlich Syndrome
Abstract
Mullerian duct anomalies have an incidence of 2–3%. Uterus didelphys belongs to Class III, according to American Fertility Society classification of Mullerian duct anomalies. Here we present a rare case of Mullerian duct anomaly-OHVIRA syndrome or HERLYN WERNER WUNDERLICH SYNDROME which is probably a new variant. An unmarried female with primary amenorrhoea presented to our department with complains of pain abdomen, referred from private hospital for hysterectomy. On investigating her, she was diagnosed to have HERLYN WERNER WUNDERLICH SYNDROME. Further management depends on understanding the imaging findings, in conjunction with the clinical presentation and opinion of experts which is critical for prevention of complications such as endometriosis or adhesions. Management depends on the presence or absence of an outflow tract obstruction.
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