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A Rare Case of Ohvira / Herlyn Werner Wunderlich Syndrome

Sudharsini T S AND Poovathi .

Abstract


Mullerian duct anomalies have an incidence of 2–3%. Uterus didelphys belongs to Class III, according to  American Fertility Society classification of Mullerian duct anomalies. Here we present a rare case of Mullerian duct   anomaly-OHVIRA  syndrome or  HERLYN WERNER WUNDERLICH SYNDROME which is probably a new  variant. An unmarried female with primary amenorrhoea   presented to our department with complains of pain   abdomen, referred from private hospital for hysterectomy.   On investigating her, she was diagnosed to have HERLYN WERNER WUNDERLICH SYNDROME.  Further management depends on understanding the imaging findings, in   conjunction with the clinical presentation and opinion of   experts which is critical for prevention of  complications  such as endometriosis or adhesions.  Management depends on   the presence or absence of an outflow tract obstruction.


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References


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